Nutrition in Cystic Fibrosis

Nutritional therapies have been key early interventions, and remain central to the well-being and survival of patients with cystic fibrosis. The nature of the disease causes significant alterations in a patient-s ability to process and assimilate nutrients.  Furthermore, many factors contribute to higher metabolic demands throughout a patient-s life. In combination, maldigestion, malabsorption, and increased metabolic demands pose a high hurdle for the patient to overcome in order to maintain optimal nutritional status.Nutrition in Cystic Fibrosis: A Guide for Clinicians is an excellent resource for physicians, nurses and dietitians who deliver care for patients with cystic fibrosis. The book provides an introduction to cystic fibrosis and nutritional assessments. It will also serve as a comprehensive guide to the nutritional monitoring and management of patients with cystic fibrosis including special populations within cystic fibrosis that require additional considerations. The chapters are written by experts in their fields and include the most up to date scientific and clinical information.Nutrition in Cystic Fibrosis: A Guide for Clinicians targets pediatric and adult pulmonologists and gastroenterologists, residents and fellows, internists, pediatricians, nurses, dietitians and general practitioners who treat patients with cystic fibrosis.

1. What is Cystic Fibrosis? The relationship between nutrition and outcomes in cystic fibrosisBy Danielle Usatin, MD and Elizabeth Yen, MD2. Macronutrient RequirementsBy Jaclyn Brownlee, RD, CNSC3. Dietary fat and fat metabolism in CFBy Asim Maqbool, MD and Birgitta Strandvik, MD, PhD4. Vitamin D and Bone HealthBy Jessica A. Alvarez, PhD, RD and Vin Tangpricha, MD, PhD5. Vitamins and MineralsBy Suzanne H. Michel and Donna H. Mueller6. Nutrition in InfancyBy Evans Machogu, MBChB, MS and Tami Miller, RD, CSP, CD7. Nutritional Assessment - Age 2-20 yearsBy Karen Maguiness, MS, RD, CSP and Molly Bozic, M.D.8. Nutrition Assessment: Adults and ObesityBy Judith A. Fulton, MPH, RD, LDN and Alexandra W.M. Wilson, MS RDN, CDE9. Nutrition InterventionBy Ala K Shaikhkhalil, MD, Suzanne Michel, MPH, RD, LDN, Maria Mascarenhas, MBBS, Virginia A Stallings, MD10. Pancreatic InsufficiencyBy Elissa Downs and Sarah Jane Schwarzenberg11. Nutrition and Cystic Fibrosis Related Liver DiseaseBy Kristin Brown RD, Cathy Lingard RD, Michael R. Narkewicz MD12. Gastrointestinal Complications of Cystic Fibrosis and their impact on NutritionBy Daniel Gelfond, MD13. Nutritional Management of Cystic Fibrosis Related Diabetes MellitusBy Katie Larson Ode, Carol Brunzell14. Nutrition Pre and Post Lung TransplantBy Teresa Schindler MS, RDN15. Pregnancy, Nutrition and Cystic FibrosisBy Michelle Brotherwood, RD, CDE16. Nutrition for Pancreatic Sufficient Individuals with Cystic FibrosisBy John F. Pohl MD and Catherine M. McDonald PhD, RDN17. Behavioral Interventions and Anticipatory Guidance By Jamie L. Ryan, PhD, Stephanie S. Filigno, PhD, and Lori J. Stark, PhD, ABPP18. Nutrition and Quality Improvement in Cystic FibrosisBy Amanda Radmer Leonard MPH, RD, CDE